Abnormally Shaped Teeth

People with MPS I generally have thick lips and an enlarged tongue. Gum ridges are broad. The teeth are widely spaced and poorly formed, and their enamel (outer layer) is fragile. It is important that the teeth be well cared for, as tooth decay can be a cause of pain. Teeth should be cleaned regularly, and if the water in your area has not been treated with fluoride, your doctor may recommend fluoride tablets or drops. Cleaning inside the mouth with a small sponge on a stick soaked in mouthwash will help keep the mouth fresh and help avoid bad breath. Even with the best dental care, an abscess around a tooth can develop because the tooth has not formed properly.

If an individual with MPS I has a heart problem, antibiotics may be given before and after any dental treatment. This is because certain bacteria in the mouth may get into the bloodstream and cause an infection in the abnormal heart valve, potentially damaging it further. Depending on the antibiotic used, side effects could differ. However, some common side effects of antibiotics include diarrhea, nausea and vomiting. Antibiotics may also cause skin rashes and allergic reactions.